关闭
产品中心

CARD9 Mouse mAb

WGD-Z-2612002
复制产品信息
Overview
别名Caspase recruitment domain-containing protein 9; hCARD9
基因名CARD9
UniProt IDQ9H257
反应种属Human
应用WB,IP,CHIP
宿主Mouse
偶联物Unconjugated
修饰Unmodified
亚型IgG1
克隆号5I4-W3-J2
克隆性Monoclonal Antibody
分子量Calculated MW: 62 kDa
纯化方式Affinity Purified
产品形式Liquid
推荐稀释比WB-1:1000; IP-1:100; CHIP-1:100
存储缓冲液Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.09% sodium azide
保存温度Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.
背景信息Caspase recruitment domain family member 9 (CARD9) is a critical adapter protein that mediates innate and adaptive immune responses, particularly against fungal pathogens. It features an N-terminal CARD domain for homophilic interactions with BCL10 and a C-terminal coiled-coil region for oligomerization. CARD9 functions as a scaffold within the CARD9-BCL10-MALT1 (CBM) complex, acting downstream of C-type lectin receptors like Dectin-1 to activate NF-κB and MAPK signaling pathways. This process triggers the production of pro-inflammatory cytokines such as TNFα and IL-6 via Syk and PKCδ. Clinically, biallelic loss-of-function mutations in CARD9 result in CARD9 deficiency, a rare autosomal recessive primary immunodeficiency. This condition is characterized by impaired Th17 immunity and extreme susceptibility to invasive fungal infections, including candidiasis and deep dermatophytosis, often presenting with central nervous system involvement.
检测原理

Copyright © 2011-2024 苏州竹子网络科技有限公司 版权所有  Sitemap 备案号:

13196813303